From: Diagnostic yield of targeted next-generation sequencing for pediatric hereditary hemolytic anemia
Characteristics | LP/P | VOUS/none | Total | P-value | |
---|---|---|---|---|---|
Age (yrs) | Â | Â | Â | Â | 0.084 |
 | N | 18 | 11 | 29 |  |
 | Median | 5 | 14 | 8 |  |
 | IQR | 6.75 | 18 | 11.5 |  |
Gender, n (%) | Â | Â | Â | 0.125 | |
 | Female | 9 (50.0) | 9 (81.8) | 18 (62.1) |  |
 | Male | 9 (50.0) | 2 (18.2) | 11 (37.9) |  |
Hb (g/dL) | Â | Â | Â | Â | 0.794 |
 | N | 18 | 11 | 29 |  |
 | Mean (SD) | 10.03 (1.99) | 10.25 (2.28) | 10.11 (2.11) |  |
Reticulocyte (%) | Â | Â | Â | 0.146 | |
 | N | 17 | 8 | 25 |  |
 | Mean (SD) | 9.35 (4.54) | 6.07 (6.16) | 8.57 (5.15) |  |
Reticulocyte count (×103/µL) |  |  |  | 0.117 | |
 | N | 17 | 8 | 25 |  |
 | Mean (SD) | 323.44 (158.19) | 203.35 (200.29) | 291.94 (178.26) |  |
RDW (%) | Â | Â | Â | Â | 0.233 |
 | N | 18 | 11 | 29 |  |
 | Mean (SD) | 18.77 (3.30) | 17.16 (3.67) | 18.16 (3.50) |  |
Poikilocytosis | Â | Â | Â | 0.044 | |
 | - | 4 | 7 | 11 |  |
 | 1+ | 8 | 1 | 9 |  |
 | 2+ | 1 | 2 | 3 |  |
 | 3+ | 1 | 0 | 1 |  |
 | 4+ | 1 | 0 | 1 |  |
LDH (IU/L) | Â | Â | Â | 0.872 | |
 | N | 18 | 8 | 26 |  |
 | Mean (SD) | 348.72 (165.63) | 337.75 (154.53) | 345.35 (135.33) |  |
Total bilirubin (mg/dL)* | Â | Â | 0.106 | ||
 | N | 17 | 9 | 26 |  |
 | Mean (SD) | 2.69 (2.15) | 1.33 (1.48) | 2.22 (2.03) |  |